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Ƅ<=XР|0緝{tIDsc*'U0 @CFm 4P BIY'РU2҈3h=ApN1iAxPj/@2Z!5"֠zt4;uYZ/'gc66n6첮tǘV AU\$*K~ D"8іXX{Q\<7f[+gao0F2bFRx)K?1͟wq 旍] 85s"~ %EV\{m<M'mܾikHB5#4{)%x-SΘ`]ڬCg W(vq{U$/|0zL7U]L_>Ueβo]~Ž>CSXEMqdٍau2^'dP]`d^+]h~pX1oǀNy .*a;AMԟH/h廂jHDF(ʸ)th&h3흳beǣ>~p՛ЛgKhd4'c!inڮ ̈́ @zߏ텎d<ڮ..@ϛ3F=s0#] ځL/PFY9MQʴʴe.oWޛb*vaWvB_=Dw M_2;+K endstream endobj 33 0 obj <>stream 2024-01-30T15:24:20+08:00 2024-01-30T15:24:17+08:00 2024-01-30T15:24:20+08:00 Acrobat PDFMaker 11 Word 版 uuid:e07244ca-62bd-4bf3-b501-e425763077e3 uuid:d857e563-2270-452f-b1fc-7196d4750db6 439 application/pdf Acute Chest Syndrome and Pulmonary Embolism in Sickle Cell Disease Case Report: About one Case Admitted at the Mixed Medecine and Sickle Cell Anemia Center (M.M.SC.A) Kinshasa in the Democratic Republic of the Congo Sickle cell disease (SCD), a hereditary genetic disorder marked by abnormal circulating hemoglobin, presents a spectrum of complications necessitating collaboration among hematologists, internists, and emergency and resuscitation physicians. Chief among these complications are vaso-occlusive crises and acute thoracic syndrome, with pulmonary embolism (PE) emerging as a critical and potentially fatal manifestation. In the pediatric SCD population, the incidence of PE is likely underestimated, and documented cases are infrequent. Furthermore, clinical symptoms may overlap with those of acute chest syndrome. This paper details the case of a 22-year-old adult with SCD admitted for chest pain, respiratory distress, and rales. Pulmonary angiography revealed bilateral pulmonary emboli, primarily distal to the right pulmonary artery. Despite attempts to conduct an etiological assessment for venous thrombosis, it proved inconclusive. The patient exhibited swift improvement following the initiation of anticoagulant therapy. Alain Munganga Mukuna, Mawisa Nkemfuni Timothée, Longina Kake Roger, Ndalako Yagbanzi Noela, Vangu Payadu Christian, Nimy-Ta-Phemba Tany, Ikoko Mpembe Mimie, Kabengele Obel Benoit Adobe PDF Library 11.0 Hematology, Internal Medicine D:20240130072406 Sickle cell disease (SCD), a hereditary genetic disorder marked by abnormal circulating hemoglobin, presents a spectrum of complications necessitating collaboration among hematologists, internists, and emergency and resuscitation physicians. Chief among these complications are vaso-occlusive crises and acute thoracic syndrome, with pulmonary embolism (PE) emerging as a critical and potentially fatal manifestation. In the pediatric SCD population, the incidence of PE is likely underestimated, and documented cases are infrequent. Furthermore, clinical symptoms may overlap with those of acute chest syndrome. This paper details the case of a 22-year-old adult with SCD admitted for chest pain, respiratory distress, and rales. Pulmonary angiography revealed bilateral pulmonary emboli, primarily distal to the right pulmonary artery. Despite attempts to conduct an etiological assessment for venous thrombosis, it proved inconclusive. 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