%0 Journal Article
%T Transposici車n corregida de grandes vasos Corrected transposition of the great arteries
%A Jos谷 Rafael Escalona Aguilera
%A Alberto Ram赤rez Ramos
%A Marcia L車pez Garc赤a
%J Revista Cubana de Pediatrˋ-a
%D 2012
%I Editorial Ciencias M谷dicas
%X Se presenta una paciente de sexo femenino, de 9 a os de edad, que acude a su m谷dico de familia y se le auscult車 un soplo al examen f赤sico y sintomatolog赤a que se comportaba como una comunicaci車n interventricular. Luego de los estudios correspondientes, se permiti車 hacer el diagn車stico de transposici車n corregida de grandes vasos. La paciente ten赤a asociada una anomal赤a de Ebstein, comunicaci車n interauricular, una comunicaci車n interventricular, y una persistencia del conducto arterioso, todo lo cual agravaba su cuadro cl赤nico. Primero es intervenida quir迆rgicamente, y se cierra el ducto; de manera espont芍nea, cierra la comunicaci車n interauricular, y la anomal赤a de Ebstein parchea la comunicaci車n interventricular. La ni a desarrolla una insuficiencia cardiaca e hipertensi車n pulmonar, a consecuencia de las anomal赤as asociadas. El caso es de inter谷s, ya que son pocos los publicados en la literatura internacional con esta cardiopat赤a cong谷nita asociada a otras anomal赤as estructurales del coraz車n, que modifican su historia natural. This paper presented a 9 years-old female patient, who went to the family's doctor and was physically examined to detect heart murmur and symptoms of ventricular septal defect. After the corresponding studies, the diagnosis was the corrected transposition of the great arteries. The patient also suffered Ebstein anomaly, atrial septal defect, ventricular septal defect and persistence of arteriose duct, all of which worsened her clinical picture. First, she was operated on and the duct was closed. Later the atrial septal defect closed spontaneously, and the Ebstein anomaly patched the ventricular septal defect. The girl developed heart failure and pulmonary hypertension, as a result of associated anomalies. The case is interesting since few cases like this one, associated with other structural heart anomalies that change its natural course, are presented in the international literature.
%K transposici車n de grandes vasos corregida
%K anomal赤a de Ebstein
%K corrected transposition of the great arteries
%K Ebstein anomaly
%U http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S0034-75312012000300012