%0 Journal Article %T Tumor rabdoide/teratoide at¨ªpico del sistema nervioso central: Presentaci¨®n de un caso Atypical teratoid/rhabdoid tumor of the central nervous system: Case report %A Jos¨¦ Mart¨ªn Bernal %A Grover Hinojosa Guzm¨¢n %A Enrique Jos¨¦ Mc Guire %A Federico Carlos Miranda %J Revista Argentina de Radiolog¨ªa %D 2012 %I Sociedad Argentina de Radiolog¨ªa %X Reportamos un caso de tumor rabdoide/teratoide at¨ªpico del sistema nervioso central (SNC) en un paciente de sexo masculino, de 20 a os de edad, que se encontraba en tratamiento m¨¦dico desde hac¨ªa seis a os por diagn¨®stico de epilepsia. Concurri¨® a nuestro hospital para realizarse una resonancia magn¨¦tica (RM), en la cual se visualiz¨® una lesi¨®n lobulada de 10 cm de di¨¢metro m¨¢ximo en la l¨ªnea media de la regi¨®n frontal. Los tumores rabdoides/teratoides at¨ªpicos del sistema nervioso central son infrecuentes y s¨®lo unos pocos casos fueron reportados en pacientes adultos. We report a case of atypical teratoid/ rhabdoid tumor of the central nervous system in a 20 year-old male, who was under treatment for epilepsy since six years ago. The patient presented at our hospital for magnetic resonance imaging (MRI), which demonstrated a midline lobulated frontal lesion with a maximum diameter of 10 cm. Atypical teratoid/rhabdoid tumors of the central nervous system are infrequent and only a few cases have been reported in adult patients. %K Resonancia magn¨¦tica %K Tomograf¨ªa computada %K Tumor rabdoide %K Tumor cerebral %K Magnetic resonance imaging %K Computed tomography %K Rhabdoid tumor %K Brain tumor %U http://www.scielo.org.ar/scielo.php?script=sci_arttext&pid=S1852-99922012000400003