颈部异位嗜铬细胞瘤十分罕见。作者报道了一例57岁的男性患者，因“发现左颈部肿块6年，头痛眩晕、胸闷胸痛9天”入院。入院时血压大幅度波动，每隔数分钟波动在200/100 mmHg~80/50 mmHg的范围。左颈部肿块进行性增大5年余。血浆17-羟皮质类固醇和17-酮类固醇正常，24小时尿VMA升高(82.7 umol/day (<68.6))。颈部的CT平扫和增强显示左侧颈部一个4.6 × 3.2 cm大小的肿块。充分的术前准备后行左颈部肿块切除术。手术顺利，无术后并发症。病理和免疫组化显示为左侧颈部异位嗜铬细胞瘤。

Ectopic pheochromocytoma in neck is rare. We reported a 57-year-old male patient who was admitted to hospital because of a mass in left neck for 6 years with headache, dizziness, chest tightness and chest pain for 9 days. He had an alternation of fluctuation of blood pressure between 200/100 - 80/50 mmHg in every several minutes. The mass progressively enlarges for more than 5 years in his left side of neck. His plasma 17-hydroxy corticosteroid and 17-ketosteroid levels were normal. The 24 hours urine VMA level was high (82.7 umol/day (<68.6)). Cervical com- puted tomography scans and enhanced scans revealed a 4.6 × 3.2 cmmass in the left side of neck. Neck mass resection was performed successfully with sufficient preoperation preparation and had no postoperative complications. Histology and immunohistochemistry of the tumor were consistent with pheochromocytoma.