%0 Journal Article %T Dyskeratosis congenita: a rare case report %A Banasree Roy %A Gobinda Mondal %A Dilip Kumar Paul %A Abul Kalam %A Kausambi Basu %J Journal of Nepal Paediatric Society %P 223-226 %D 2013 %I Nepal Paediatric Society %R 10.3126/jnps.v33i3.8166 %X Dyskeratosis congenita is a rare congenital disorder affecting mainly the integumentary system. It is a progressive disease with involvement of bone marrow. A triad of hyperpigmentation, nail dystrophy and leucoplakia are characteristic of this disease. DOI: http://dx.doi.org/10.3126/jnps.v33i3.8166   J. Nepal Paediatr. Soc. 2013;33(3):223-226 %K Hyperpigmentation %K nail dystrophy %K leucoplakia %U http://www.nepjol.info/index.php/JNPS/article/view/8166