%0 Journal Article %T Retroperitoneal Extrarenal Angiomyolipomas: An Evidence-Based Approach to a Rare Clinical Entity %A Emmanuel J. Minja %A Megan Pellerin %A Nicole Saviano %A Ronald S. Chamberlain %J Case Reports in Nephrology %D 2012 %I Hindawi Publishing Corporation %R 10.1155/2012/374107 %X Extrarenal angiomyolipomas (ERAMLs) are rare tumors that present as incidentalomas upon imaging for other conditions. Retroperitoneal ERAMLs present a unique challenge from a diagnostic and treatment standpoint as they can mimic other benign and malignant retroperitoneal tumors. We present a case of a 39-year-old female with a 19.3 cm × 13.5 cm × 10.7 cm left extrarenal retroperitoneal mass. Histopathologic examination and HMB-45 staining revealed the mass to be a retroperitoneal ERAML. Our case report provides a comprehensive literature review and an evidence-based algorithm for taking care of patients with ERAMLs. %U http://www.hindawi.com/crim/nephrology/2012/374107/