%0 Journal Article
%T A Case of Mayer每Rokitansky每K邦ster每Hauser Syndrome with a Fused Pancake-shaped Pelvic Kidney
%A Ali Reza Eftekhari Moghadam
%A Ghasem Saki
%A Mahin Taheri Moghadam
%A Mohammad Hossein Jamshidi
%A Seyed Mohamad Hossein Mohseni
%A Vajieh Heidari
%J Archive of "Advanced Biomedical Research".
%D 2019
%R 10.4103/abr.abr_97_18
%X Mayer每Rokitansky每K邦ster每Hauser (MRKH) Syndrome is a female reproductive system disorder. It is characterized by a defect in the M邦llerian ducts development, and it causes the absence of the uterus in variable degrees in upper vaginal hypoplasia. In addition, it is often associated with the unilateral renal dysplasia. M邦llerian agenesis affects 1 in 4500 newborn girls and is considered as a sporadic anomaly. Women with MRKH Syndrome have a normal female chromosome pattern 46, XX with normal ovarian function. The presence of bilateral kidney agenesis with a pelvic pancake-shaped kidney is a rare condition, and a few cases have been reported in medical journals. This case study focuses on a case of MRKH Syndrome with bilateral renal agenesis and a pancake-shaped kidney
%K Mayer每Rokitansky每K邦ster每Hauser Syndrome
%K M邦llerian ducts
%K renal agenesis
%U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6543865/