%0 Journal Article %T Linear scleroderma ¡°en coup de sabre¡± with extensive brain involvement¡ªClinicopathologic correlations and response to anti-Interleukin-6 therapy %A Cynthia M. Magro %A Ilya Kister %A Lee Shapiro %A Luke C. Olson %A Pierre Halteh %J Archive of "Orphanet Journal of Rare Diseases". %D 2019 %R 10.1186/s13023-019-1015-7 %X Clinical Images. a There is a striking linear area of alopecia and induration involving the vertex of the scalp defining a classic presentation of en coup de sabre. Additional areas of induration are present over the left superior back (b) and over the left distal medial left thigh (c %K Linear scleroderma %K ¡°en coupe de sabre %K ¡± vasculitis %K Autoimmune endotheliopathy %U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6524280/