%0 Journal Article
%T A rare case of an isolated aneurysmal supravalvar mitral ring in a young Nigerian adult: a cor-triatriatum mimic
%A Michael Akinkunmi
%A Ogochukwu Sokunbi
%A Oyewole A Kushimo
%A Yeside O Akinbolagbe
%J Archive of "Oxford Medical Case Reports".
%D 2019
%R 10.1093/omcr/omz050
%X Supravalvar mitral ring is a rare congenital abnormality characterized by a ridge of connective tissue located above the mitral valve. It is a cause of congenital mitral stenosis typically presenting in childhood and usually associated with other cardiac abnormalities. We report the rare case of a 24-year-old male presenting with an isolated aneurysmal supravalvar mitral ring. He presented at the emergency room with a 2-week history of worsening heart failure symptoms and antecedent effort intolerance of 4 years duration. He was referred from a primary care facility with an echo diagnosis of cor-triatriatum. Echocardiography done at our centre revealed an isolated aneurysmal supravalvar mitral ring of the intramitral variant. This report highlights the unusual isolated presentation of a supravalvar mitral ring in a young adult and the need to carefully differentiate it from cor-triatriatum, a possible close mimic
%U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6600123/