%0 Journal Article
%T Primary Extraskeletal Osteosarcoma Arising from the Optic Nerve: A Rare Case Report
%A Arindom Kakati
%A Bifica Lyngdoh
%A Biswajit Dey
%A Caleb Harris
%A Evarisalin Marbaniang
%A Jaya Mishra
%A Rintu Marak
%A Zachariah Chowdhury
%J Archive of "Ocular Oncology and Pathology".
%D 2018
%R 10.1159/000486420
%X Orbital location of extraskeletal osteosarcoma is extremely rare with only 4 cases reported so far in the English literature. We present the case of a 32-year-old female who presented with proptosis and complete loss of vision of the left eye. Contrast-enhanced computed tomography scan showed a densely calcified lobulated lesion in the left optic nerve showing strong enhancement. A left fronto-occipito-zygomatic osteotomy was conducted and a greyish brown tumor was identified. Histopathological and immunohistochemical examination of the curetted material revealed it to be extraskeletal osteosarcoma. A left partial maxillectomy with ethmoidectomy and left orbital exenteration was done and the patient was advised chemotherapy with radiotherapy
%K Osteoid
%K Orbit
%K Vimentin
%U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6167680/