%0 Journal Article %T Congenital Nasal Dermoid Sinus Cyst in Children %J - %D 2018 %X Background: Nasal dermoid sinus cyst is a rare congenital anomaly affecting approximately 1 in 20,000¨C40,000 live births. It is liable for infection and may communicate with the central nervous system. The treatment is complete surgical excision. Case history: Nine months old male presented by a pea-size fronto-nasal swelling over the nasal bridge since birth, gradually increasing in size with recent history of local redness and discharge. Sagittal CT of the skull showed osteolytic lesion at the fronto-nasal bone with eroded inner and outer tables). MRI showed no intracranial extension. Surgical excision was done by combined nasal and bicoronal incisions. A big abscess cavity was encountered at the fronto-nasal bone junction. The diagnosis of Nasal dermoid sinus cyst was confirmed by histopathology. The patient was followed in the outpatient clinic; MRI was done after one month. No recurrence was detected %K Congenital Midface Anomalies %K Nasal Dermoid %K Frontonasal Swelling %U http://www.sciencepublishinggroup.com/journal/paperinfo?journalid=265&doi=10.11648/j.ijcd.20180101.12