%0 Journal Article
%T AA Amyloidosis Secondary to Primary Sjögren Syndrome: Can It Be Developed without Chronic Inflammation?
%A Soukaina Zaher
%A Kawtar Nassar
%A Ibtissam Razzouki
%A Meriem Regragui
%A Mehdi Karkouri
%A Saadia Janani
%J Open Journal of Rheumatology and Autoimmune Diseases
%P 29-35
%@ 2164-005X
%D 2021
%I Scientific Research Publishing
%R 10.4236/ojra.2021.112004
%X <div style=\"text-align:justify;\">
	<span style=\"font-family:Verdana;\"><strong>Background:</strong> The association of primary Sj<span style=\"white-space:nowrap;\">&amp;#246;</span>gren syndrome (PSS) and AA amyloidosis is a rare occurrence. <strong>Objective: </strong>To describe the phenotype of patients with this association through our two cases and a literature review. <strong>Materials and methods:</strong> A report of two cases of AA amyloidosis complicating primary Sj<span style=\"white-space:nowrap;\">&amp;#246;</span>gren syndrome with a literature review. <strong>Results:</strong> Eight patients of Primary Sj<span style=\"white-space:nowrap;\">&amp;#246;</span>grenĄ¯s Syndrome complicated by AA amyloidosis were studies. Six cases were reported in the literature by consulting several databases. 50% of patients had a positive immunological assessment, three cases with kidney damage, and three cases lung damage. <strong>Conclusion: </strong>The immunological activity in the Primary SjogrenĄ¯s Syndrome requires the search not only a lymphoma but also AA amyloidosis apart from any clinical or biological chronic inflammation.</span> 
</div>
%K AA Amyloidosis
%K Amyloid
%K Primary Sj&#246
%K gren Syndrome
%U http://www.scirp.org/journal/PaperInformation.aspx?PaperID=108600