%0 Journal Article
%T Macrophage Activation Syndrome as the Primary Presentation of Pediatric Systemic Lupus Erythematosus: A Case Report and Review of the Literature
%A Hanane Hajaj
%A Hanae Bahari
%A Aziza El Ouali
%A Ayyad Ghanam
%A Maria Rkain
%A Abdeladim Babakhouya
%J Open Journal of Pediatrics
%P 132-138
%@ 2160-8776
%D 2024
%I Scientific Research Publishing
%R 10.4236/ojped.2024.141014
%X Macrophage activation syndrome (MAS), in its secondary form, often
complicates rheumatic diseases but rarely constitutes a mode of revelation.
Systemic lupus erythematosus (SLE) is a systemic autoimmune disease of unknown
etiology that primarily affects women in adulthood. MAS is a serious condition
that may be the first presentation of SLE. Here, we report the case of a
4-year-old female with MAS as the primary manifestation of Systemic Lupus
Erythematosus (SLE). In this case, we outline the characteristics of a complex
case of SLE that was initially accompanied with MAS, and also review the
literature to discuss the clinical, biological, and therapeutic aspects of this
condition.
%K Macrophage Activation Syndrome
%K Systemic Lupus Erythematosus
%K Child
%U http://www.scirp.org/journal/PaperInformation.aspx?PaperID=130658