%0 Journal Article
%T Desmoplastic small round cell tumor of the abdomen
%A Andr¨¦s
%A R.
%A Mayordomo
%A J. I.
%A Isla
%A D.
%A Ram¨®n y Cajal
%A S.
%A Tejero
%A E.
%A Navarro
%A A.
%A Polo
%A E.
%A Lastra
%A R.
%A Ortega
%A E.
%A Ruiz-Echarri
%A M.
%A Lozano
%A R.
%A Tres
%A A.
%J Oncolog¨ªa (Barcelona)
%D 2006
%I Scientific Electronic Library Online
%R 10.4321/S0378-48352006000200004
%X a 21-year old woman presented with a 2-month history of abdominal pain. the diagnostic work-up disclosed a 17-cm intraperitoneal mass. biopsy showed islets containing small round cells surrounded by abundant desmoplastic stroma. immunohistochemistry was strongly positive for desmin and weakly positive for vimentin and neuron-specific enolase. pathological diagnosis was intraabdominal round cell desmoplastic tumor. the patient underwent an intensive schedule of high-dose alkylator-based chemotherapy, the p6 protocol, designed by the pediatrics division of the memorial sloan-kettering cancer center. she had a partial response and subsequently underwent resection of the residual mass followed by high-dose chemotherapy with stem cell support. ten months later, the patient had disease progression and is currently receiving second-line chemotherapy.
%K desmoplastic small
%K round cell tumor
%K high-dose chemotherapy
%K intrabdominal tumor.
%U http://scielo.isciii.es/scielo.php?script=sci_abstract&pid=S0378-48352006000200004&lng=en&nrm=iso&tlng=en