Anestesia en la neurofibromatosis tipo 1. A propósito de un caso

introduction: the type 1 neurofibromatosis or von recklinghausen's neurofibromatosis is the more frequent neurocutaneous disorder, present in approximately 1 of each 3000 persons. it is a genetic syndrome with an autosomal dominant way of transmission. criteria for the clinical diagnosis were made in 1988, from two or more spots of white coffee color larger than 5 millimeters diameter in postpubertal subjects, two or more neurofibroma of any type or a plexiform neurofibroma, axillary freckles or in the inguinal region, optical glioma; two or more lisch's nodules, bone lesions such as sphenoid dysplasia or a thin cortex of large bones with or without pseudoarthrosis, as well as a first grade relative blood relation diagnosed with type 1 neurofibromatosis. objective: to present the operative behavior of patients presenting with type 1 neurofibromatosis. clinical case: ira white male patient aged 71 with a pathologic history of type 1 neurofibromatosis diagnosed from 15 years old with a left heart insufficiency, high blood pressure and chronic auricular fibrillation with a normal ventricular response. diagnosis of lumbar neurofibroma was made carrying out a total exeresis of the lesion. conclusions: the peri-anesthetic conduction of patient diagnosed with von recklinghausen's disease is a challenge for the anesthesiologist.