Sequential Bilateral Lenticulo-Corneal Touch in a Patient with Weill-Marchesani Syndrome

PURPOSE: To report a case of Weill-Marchesani syndrome (WMS) with spontaneous sequential bilateral lenticulo-corneal touch, a previously unreported finding in this condition. CASE REPORT: A 26-year-old woman, a known case of WMS, presented with central lenticulo-corneal touch and corneal edema but normal intraocular pressure (IOP) and a patent laser iridotomy in her left eye. She underwent lensectomy, anterior vitrectomy and iris claw-fixated aphakic intraocular lens implantation. Seven days later a similar presentation developed in her right eye which underwent a similar procedure. Seven months postoperatively, best corrected visual acuity was 20/25, IOP was normal and the corneas were clear in both eyes; central corneal thickness was 555 and 573 μm in the right and left eyes, respectively. Ocular examinations were otherwise unremarkable. CONCLUSIONS: Spontaneous lenticulo-corneal touch is a previously unreported finding in Weill-Marchesani syndrome.