PREGNANCY OUTCOME IN POST SPLENECTOMY PATIENT WITH HEREDITARY SPHEROCYTOSIS – A CASE REPORT

Hereditary spherocytosis (HS) is a rare type of hemolytic anemia in southeast-Asian population whereas it is common among western countries like north Europe. Hereditary Spherocytosis (HS) is most common red cell membrane disorder with varying degrees of clinical severity, membrane protein defect and modes of inheritance. In majority of cases transmission is autosomal dominant .Severity of the disease is classified as mild, moderate and severe forms. 3-5% of the patients have severe disease and often complicated by cholelithiasis. Though severe form is an indication for splenectomy presently evidence favouring the conservative approach to splenectomy. There are only few case report series concerning the pregnancy complicated by HS. Though hemolytic crisis was managed conservatively in some cases, outcome of pregnancy was more favorable after splenectomy than before. We report a case of HS with post splenectomy complicated pregnancy with good maternal and fetal outcome