Granulomatosis with Polyangiitis Presenting with Bilateral Hearing Loss and Facial Paresis

Granulomatosis with polyangiitis (GPA) is a rare vascular inflammatory disease that affects the upper and lower respiratory tract and kidneys. Although the etiology of GPA is unknown, it is thought to be triggered by environmental events among patients with genetic susceptibility.1 Due to the frequency of upper respiratory tract involvement (70%-100%), otorhinolaryngologic symptoms may be the first clinical manifestation of disease.