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- 2019
Desensitization in patients with hypersensitivity to haem arginate: A case reportDOI: 10.1016/j.waojou.2018.11.002 Keywords: Porphyria, Hypersensitivity to haem arginate, Hemin arginate Abstract: Porphyria comprises a group of metabolic disorders caused by the irregular activities of enzymes within the haem biosynthetic pathway. This disease can provoke a large variety of symptoms. Acute porphyria attacks need to be treated urgently to avoid prolonged illness and fatal complications. Haem arginate, a concentrated haem solution stabilized with arginine, is the only preparation available for treatment in Europe and South America. This report describes a safe desensitization protocol for patients who require such treatment and have haem arginate hypersensitivity
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