Introduction and objective: Hemophilia is a genetic bleeding disorder inherited as a recessive train linked
to the male gender.Bleeding into the central nervous system in patients with hemophilia is
an extremely dangerous condition that can be directly life-threatening, if left
untreated. Extradural hematoma of the
dorso-lumbar region is rare but potentially deadly disease in children. This condition can result in severe neurological deficits. We aim to discuss the clinical, radiological and
progressive clinical aspects of this illness. Case report: We report the case of a5-year-old child with severe hemophilia A treated
for extradural hematoma of the
dorso-lumbar region resulting from trauma. A spinal magnetic resonance
imaging revealed an extradural hematoma. The patient was successfully treated
with intensive replacement therapy and did not require surgical
References
[1]
Agrawal, D. and Mahapatra, A.K. (2003) Spontaneous Subdural Hematoma in a Young Adult with Hemophilia. Neurology India, 51, 114-115.
[2]
Kiehna, E.N., Waldron, P.E. and Jane, J.A. (2010) Conservative Management of an Acute Spontaneous Holocord Epidural Hemorrhage in a Hemophiliac Infant. Journal of Neurosurgery, 6, 43-48. https://doi.org/10.3171/2010.4.PEDS09537
[3]
Cromwell, L.D., Kerber, C. and Ferry, P.C. (1977) Spinal Cord Compression and Hematoma: An Unusual Complication in a Hemophiliac Infant. American Journal of Roentgenology, 128, 847-849. https://doi.org/10.2214/ajr.128.5.847
[4]
Franchini, M. and Mannucci, P.M. (2012) Past, Present and Future of Hemophilia: A Narrative Review. Orphanet Journal of Rare Diseases, 7, Article No. 24.
https://doi.org/10.1186/1750-1172-7-24
[5]
Boyadzhiev, D. and Dumitriu, D. (2019) A Rare Case of Back Pain in a 4 Month-Old Baby with Type A Hemophilia. Journal of the Belgian Society of Radiology, 103, 46. https://doi.org/10.5334/jbsr.1804
[6]
Hoyer, L.W. (1994) Hemophilia A. The New England Journal of Medicine, 330, 38-47. https://doi.org/10.1056/NEJM199401063300108
[7]
Hutt, P.J., Herold, E.D., Koenig, B.M. and Gilchrist, G.S. (1996) Spinal Extradural Hematoma in an Infant with Hemophilia A: An Unusual Presentation of a Rare Complication. The Journal of Pediatrics, 128, 704-706.
https://doi.org/10.1016/S0022-3476(96)80141-7
[8]
Bisson, E.F., Dumont, T. and Tranmer, B. (2007) Spontaneous Spinal Epidural Hematoma in a Child with Hemophilia B. Canadian Journal of Neurological Sciences, 34, 488-490. https://doi.org/10.1017/S0317167100007423
[9]
Pai, S.B. and Maiya, P.P. (2006) Spontaneous Spinal Epidural Hematoma in a Toddler: A Case Report. Child’s Nervous System, 22,526-529.
https://doi.org/10.1007/s00381-005-0002-6
[10]
Borkar, S.A., Prasad, G.L., Satyarthee, G.D. and Mahapatra, A.K. (2011) Spontaneous Spinal Extradural Hematoma in a Child with Hemophilia B, Surgery or Medical Management—A Dilemma? Journal of Pediatric Neurosciences, 6, 131-133.
[11]
Starobrat, G., Taczała, J., Fatyga, M., et al. (2019) Posttraumatic Epidural Hematoma in a Child with Severe Hemophilia A—Case Study. Journal of Pre-Clinical and Clinical Research, 13, 76-78. https://doi.org/10.26444/jpccr/106100
