Congenital radio-ulnar synostosis (CRUS) is a rare skeletal malformation
of the upper limb and the most common congenital functional disorder of the
elbow joint, causing limitation in forearm rotational movements, which may lead
to difficulties with some activities of daily living. We reported a 4-year-old girl with congenital bilateral proximal radio-ulnar synostosis who
presented with functional discomfort due to limitation of the prono-supination
movements of the forearms and abnormal gestures when handling objects. She has
clinical and radiological features of congenital radio-ulnar synostosis (CRUS).
However, the parents declined corrective surgery because of wrong perception of
the condition to be normal. This case highlighted the poor health seeking
behavior and wrong illness perception prevalent in the developing countries.
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