The newborn infant presented with severe proptosis. Data on clinical history,
presentation, photos, radiological imaging, and laboratory results were presented.
A literature review was conducted for the case and relevant treatment modalities.
The surgical technique and the outcome were also discussed. The mass was
present since birth in a full term neonate, causing complete globe dislocation
of the left eye. Imaging showed a large cystic
retro-bulbar mass completely occupying the orbital cavity and causing anterior
dislocation of the left globe. Surgical excision of the tumor was carried out with
globe preservation and Histopathology examination confirmed the diagnosis of optic
nerve glioma. This was an atypical presentation of an optic nerve glioma
causing globe dislocation in a neonate. The resection of such a large orbital
tumor made globe preservation possible and resulted in an excellent cosmetic
outcome.
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