Hipertensión pulmonar asociada a neurofibromatosis

pulmonary hypertension secondary to systemic disease belongs to a partnership including in the latest guidelines for diagnosis and treatment of pulmonary hypertension of the european society of cardiology, but given the heterogeneity and rarity, there is nopathophysiological support. we report a patient with pulmonary hypertension associated with neurofibromatosis without other etiology demonstrated