Síndrome de Moyamoya y complicaciones neurológicas en un paciente con enfermedad de células falciforme

sickle cell disease, although infrequent, is a disease with high comorbidity, stroke and vascular malformations by endothelial deformity are major and catastrophic complications in patients with sickle cell disease, which is why proper monitoring of these patients can prevent the high rate of complications that this disease leads. the situation of a 24 years old african-american woman with sickle cell disease and several strokes during adolescence is exposed. the patient had a complicated pregnancy due to secondary intraventricular hemorrhage and multiple vascular malformations type moyamoya. she developed a convulsive status epilepticus and an irreversible neurological impairment.