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Slight OSAS (apnoea-hypopnoea index (AHI) was 1.5 - 5) was diagnosed in 4 patients (23.5%), moderate OSAS (AHI was 5 - 10)—in 4 patients (23.5%), severe OSAS (AHI was higher than 10)—in 2 patients (11.8%). AHI median at Hunter syndrome was 5.3 ± 6.9/ hour. In the group of infants (1 - 3 years old) slight OSAS (AHI is 0.8 ± 0.3/h) dominated, whereas in the group of teenagers—sever OSAS (AHI is 10.9 ± 9.4/h), a median of blood saturation with oxygen (SpO2) was 87.5 ± 10.6%, desaturation index (DI)—10.4 ± 13.3/hour. On the whole, OSAS was diagnosed in 58.8% of children and increased with increasing of the disease severity. Thus cardiorespiratory monitoring is necessary for revealing children with moderate and moderate-to-severe OSAS, followed by prevention of life-threatening conditions, the occurrence of which is possible at this syndrome. A. A. Baranov, L. S. Namazova-Baranova, N. D. Vashakmadze, A. K. Gevorkyan, L. M. Kuzenkova, T. V. Podkletnova, O. V. Kozhevnicova, B. B. Altunin Adobe PDF Library 11.0 Hunter Syndrome, Mucopolysaccharidoses, Cardiorespiratory Monitoring, Obstructive Sleep Apnea Syndrome D:20150625111542 In order to assess the prevalence and dynamics of changes of basic parameters of obstructive sleep apnea syndrome (OSAS) at mucopolysaccharidoses II (MSP II) cardiorespiratory monitoring was performed for 17 children. Slight OSAS (apnoea-hypopnoea index (AHI) was 1.5 - 5) was diagnosed in 4 patients (23.5%), moderate OSAS (AHI was 5 - 10)â•flin 4 patients (23.5%), severe OSAS (AHI was higher than 10)â•flin 2 patients (11.8%). AHI median at Hunter syndrome was 5.3 ± 6.9/ hour. In the group of infants (1 - 3 years old) slight OSAS (AHI is 0.8 ± 0.3/h) dominated, whereas in the group of teenagersâ•flsever OSAS (AHI is 10.9 ± 9.4/h), a median of blood saturation with oxygen (SpO2) was 87.5 ± 10.6%, desaturation index (DI)â•fl10.4 ± 13.3/hour. On the whole, OSAS was diagnosed in 58.8% of children and increased with increasing of the disease severity. Thus cardiorespiratory monitoring is necessary for revealing children with moderate and moderate-to-severe OSAS, followed by prevention of life-threatening conditions, the occurrence of which is possible at this syndrome. endstream endobj 30 0 obj <>stream h220W0Pw/+QL)624)@H0i1PLT$ endstream endobj 31 0 obj <>stream hބTn;;MUV ! j4HD=7ܘ+ \mdž 爕77?%CHv61sÕ޶9ϼz;sކ & pM-fptV?{`0bS܅[V,gVR+]V\5-ZNj5[zI:H.ztԻ\I,2\,D)6 D) lL$"0q6¶kQNLWh,ϲ)Eۆ+nm%T+I ֤pi3'qaT?)͌uT$S4eIܝdH8r%QG+fu([bo-/Pe\ ,Pư\r+3JĄ3}u<uhE A M3ZY"1*4+mJ@^CYZ܁HDD#M Z FWkʣlvB"Rlᜤ:Y"nJU) AW&h^D׃|SOA$[!М<ႍSG0r򮍮+_-8S+~%}hB2`K'-$lH ws2ԋ66RP,CT|M?K6";xmO|Z &9Ak֨a^u^Rپ{Wmx#վ#{28庠^~0[a,ʼb2 [ߗ^6a i5 wKSNf4~}G("/1xwl>/Filter/FlateDecode/ID[<2FCA26142D20F34594A1CF8B235C3C49><30BAFB89BFF5284C8471FDDB93946BD6>]/Info 208 0 R/Length 173/Root 210 0 R/Size 209/Type/XRef/W[1 3 1]>>stream hbb&F&i>&FvD2OHi!ɔ"G"b`]?"`q Rs*XDH22@/dp ,"Y]uDJق,*G.|hjz]ðK(5zߙހ` endstream endobj startxref 116 %%EOF 29 0 obj <>stream 2015-06-25T19:28:04+08:00 2015-06-25T19:26:57+08:00 2015-06-25T19:28:04+08:00 Acrobat PDFMaker 11 Word 版 uuid:14324b63-26de-45b4-9e01-d4b9d614444c uuid:5758f0bc-76d9-4613-b73d-4105f5bdc474 392 application/pdf Obstructive Sleep Apnea Syndrome in Children with Mucopolysaccharidoses II (Hunter Syndrome) In order to assess the prevalence and dynamics of changes of basic parameters of obstructive sleep apnea syndrome (OSAS) at mucopolysaccharidoses II (MSP II) cardiorespiratory monitoring was performed for 17 children. Slight OSAS (apnoea-hypopnoea index (AHI) was 1.5 - 5) was diagnosed in 4 patients (23.5%), moderate OSAS (AHI was 5 - 10)—in 4 patients (23.5%), severe OSAS (AHI was higher than 10)—in 2 patients (11.8%). AHI median at Hunter syndrome was 5.3 ± 6.9/ hour. In the group of infants (1 - 3 years old) slight OSAS (AHI is 0.8 ± 0.3/h) dominated, whereas in the group of teenagers—sever OSAS (AHI is 10.9 ± 9.4/h), a median of blood saturation with oxygen (SpO2) was 87.5 ± 10.6%, desaturation index (DI)—10.4 ± 13.3/hour. On the whole, OSAS was diagnosed in 58.8% of children and increased with increasing of the disease severity. Thus cardiorespiratory monitoring is necessary for revealing children with moderate and moderate-to-severe OSAS, followed by prevention of life-threatening conditions, the occurrence of which is possible at this syndrome. A. A. Baranov, L. S. Namazova-Baranova, N. D. Vashakmadze, A. K. Gevorkyan, L. M. Kuzenkova, T. V. Podkletnova, O. V. Kozhevnicova, B. B. Altunin Adobe PDF Library 11.0 Hunter Syndrome, Mucopolysaccharidoses, Cardiorespiratory Monitoring, Obstructive Sleep Apnea Syndrome D:20150625111542 In order to assess the prevalence and dynamics of changes of basic parameters of obstructive sleep apnea syndrome (OSAS) at mucopolysaccharidoses II (MSP II) cardiorespiratory monitoring was performed for 17 children. Slight OSAS (apnoea-hypopnoea index (AHI) was 1.5 - 5) was diagnosed in 4 patients (23.5%), moderate OSAS (AHI was 5 - 10)â•flin 4 patients (23.5%), severe OSAS (AHI was higher than 10)â•flin 2 patients (11.8%). AHI median at Hunter syndrome was 5.3 ± 6.9/ hour. In the group of infants (1 - 3 years old) slight OSAS (AHI is 0.8 ± 0.3/h) dominated, whereas in the group of teenagersâ•flsever OSAS (AHI is 10.9 ± 9.4/h), a median of blood saturation with oxygen (SpO2) was 87.5 ± 10.6%, desaturation index (DI)â•fl10.4 ± 13.3/hour. On the whole, OSAS was diagnosed in 58.8% of children and increased with increasing of the disease severity. 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